Oral Presentation ESA-SRB-APEG-NZSE 2022

Adrenal histopathology, adrenal vein sampling results and surgical outcomes in patients with primary aldosteronism (#125)

Kartik Sehgal 1 , Renata Libianto 2 3 4 , Jinghong Zhang 5 , Pranav Dorwal 6 , Ian Simpson 6 , Winston Chong 7 , Ken Lau 1 7 , James Doery 3 6 , Simon Grodski 8 9 10 , James Lee 8 9 10 , William Rainey 11 , Peter J Fuller 2 4 , Jun Yang 2 3 4
  1. School of Clinical Sciences, Monash University, Melbourne, Victoria, Australia
  2. Department of Endocrinology, Monash Health, Melbourne, Victoria, Australia
  3. Department of Medicine, Monash University, Melbourne, Victoria, Australia
  4. Centre for Endocrinology and Metabolism, Hudson Institute of Medical Research, Melbourne, Victoria, Australia
  5. Central Clinical School, Monash University, Melbourne, Victoria, Australia
  6. Monash Pathology, Monash Health, Melbourne, Victoria, Australia
  7. Monash Imaging, Monash Health, Melbourne, Victoria, Australia
  8. Department of Surgery, Monash Health, Melbourne, Victoria, Australia
  9. Department of Surgery, Monash University, Melbourne, Victoria, Australia
  10. Monash University Endocrine Surgery Unit, Alfred Health, Melbourne, Victoria, Australia
  11. Department of Molecular and Integrative Physiology and Internal Medicine, University of Michigan, Ann Arbor, Michigan, United States of America

Primary aldosteronism caused by unilateral adrenal disease can be identified by adrenal vein sampling (AVS) and treated by adrenalectomy1. A recent study suggested that patients whose resected adrenal tissue contains a CYP11B2 (aldosterone synthase) staining adenoma (classical pathology) are more likely to be cured than those whose resected adrenal contains micronodules (non-classical pathology)2. We have reported that AVS outcomes before and after the use of ACTH stimulation can be discordant (median lateralisation index ≥ 4 pre-ACTH to <4 post-ACTH), with the loss of lateralisation post-ACTH affecting 18% of patients3. We hypothesise that AVS discordance may predict both adrenal histopathology and surgical outcomes.

 

We performed a retrospective analysis of AVS results, histopathology, and surgical outcomes in 41 patients who underwent AVS and adrenalectomy at Monash Health between 2009-2020.

 

Of the 32 patients with concordant lateralisation on AVS both pre- and post-ACTH, 9 demonstrated classical pathology, 6 had non-classical pathology and 11 had mixed pathology. 6 did not stain for CYP11B2.  18 patients achieved complete biochemical cure with a normalised aldosterone renin ratio at 3 – 12 months post-surgery, while 8 patients had missing post-operative data.  Of the 9 patients with discordant lateralisation on AVS, none had pure classic pathology while 1 had non-classical and 7 had mixed pathology. Among this group, from 5 patients with post-operative biochemical data, 4 achieved complete cure while 1 had partial cure with persistently abnormal aldosterone to renin ratio.

 

In summary, patients with concordant results pre- and post-ACTH stimulated AVS are more likely to display a CYP11B2 positive adenoma and achieve complete surgical cure. Conversely, patients with AVS discordance are more likely to display non-classical or mixed pathology and lower rates of clinical cure. Hence, ACTH stimulation may be a valuable tool in AVS to identify “falsely lateralising” PA and decrease the risk of unsuccessful surgery.

  1. Diagnosis and treatment of primary aldosteronism Reincke M, Bancos I, Mulatero P, Scholl UI, Stowasser M, Williams TA. Diagnosis and treatment of primary aldosteronism. The Lancet Diabetes & Endocrinology. 2021 Dec 1;9(12):876-92.
  2. Single-Center Prospective Cohort Study on the Histopathology, Genotype, and Postsurgical Outcomes of Patients With Primary Aldosteronism Meyer LS, Handgriff L, Lim JS, Udager AM, Kinker IS, Ladurner R, Wildgruber M, Knösel T, Bidlingmaier M, Rainey WE, Reincke M. Single-Center Prospective Cohort Study on the Histopathology, Genotype, and Postsurgical Outcomes of Patients With Primary Aldosteronism. Hypertension. 2021 May 24: HYPERTENSIONAHA-121
  3. Utility of adrenocorticotropic hormone in adrenal vein sampling despite the occurrence of discordant lateralization Chee NY, Abdul‐Wahab A, Libianto R, Gwini SM, Doery JC, Choy KW, Chong W, Lau KK, Lam Q, MacIsaac RJ, Chiang C. Utility of adrenocorticotropic hormone in adrenal vein sampling despite the occurrence of discordant lateralization. Clinical endocrinology. 2020 Oct;93(4):394-403.